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Subject: iron/myasthenia gravis
Am J Hematol 1994 Mar;45(3):260-261
Hereditary hemochromatosis and red cell aplasia.
Adams PC
Department of Medicine, University of Western Ontario, University
Hospital, London, Canada.
A 63-year-old white man with myasthenia gravis and red cell aplasia
was found to have hepatic iron overload. The differential diagnosis
included hereditary hemochromatosis and secondary iron overload
related to red cell aplasia. Family studies of siblings, including HLA
typing, initially suggested a diagnosis of secondary iron overload.
The investigation of a remote sibling led to the final diagnosis of
hereditary hemochromatosis. The case illustrates the importance of
complete family investigations in the differentiation between
hereditary hemochromatosis and secondary iron overload and the
potential hazard of using HLA typing as an indirect genetic test for
hereditary hemochromatosis.
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