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Subject: back/lumbar pain
Dtsch Med Wochenschr 1999 Jan 29;124(4):79-82
[Marked hemosiderosis in myelodysplastic syndrome].
[Article in German]
Klinz C
Abteilung Innere Medizin, Bundeswehrkrankenhaus Hamburg.
HISTORY AND ADMISSION FINDINGS: A 68-year-old man was admitted because
of symptoms of lumbar pain. He was known to have chronic anemia with
ring sideroblasts and diabetes melitus and to be in heart failure.
Three months before he had been given 7 units of red cell concentrate.
On admission the outstanding features were brown discoloration of the
skin, absent body hair, tachycardia, hepatomegaly and small testicles.
INVESTIGATIONS: He had a normocytic anemia, hyperglycemia and raised
transaminases, hypogonadism and vitamin D3 deficiency. The serum
levels of iron, transferrin saturation and feritin were markedly
elevated. Liver iron content/g dried liver was 4.2 g (by
biomagnetometer). Radiology of the lumbar vertebrae showed
osteoporosis and sonography confirmed hepatomegaly. DIAGNOSIS,
TREATMENT AND COURSE: The known myelodysplastic syndrome (MDS) had fed
to secondary hemosiderosis with heart failure, liver involvement,
diabetes mellitus, hypogonadism and osteoporosis. Symptomatic
treatment was unsuccessfully complemented by desferoxamine (up to 4
g/12 h) to release iron. But very good iron excretion was then
achieved with deferiprone (3 x 1 g/d). The patient later died of the
sequelae of hemosiderosis. CONCLUSION: Even when they have not
required transfusions, patients with long-standing MDS should be
examined regularly for the possible development of secondary
hemosiderosis so that iron-chelating agents can be administered as
needed.
PMID: 10071604, UI: 99170998
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